{"abstracts":[{"sha1":"fdc83015f6c74cb39c2ee2c80ecd1811fdf71dc3","content":"Resumo\n Objetivo Avaliar o resultado estético e funcional do tratamento cirúrgico da deformidade de Madelung em idade pediátrica.\n Método Estudo retrospectivo dos pacientes com deformidade de Madelung em idade pediátrica tratados cirurgicamente através de osteotomia em cúpula do rádio distal e secção do ligamento de Vickers entre 2015 e 2018. Foram incluídos doentes com tempo de seguimento pós-operatório mínimo de 12 meses. Foram analisados dados demográficos, técnica cirúrgica, resultados clínicos e radiográficos. A avaliação radiográfica pré e pós-operatória consistiu na medição da inclinação ulnar, do afundamento semilunar, do ângulo da fossa semilunar e do desvio palmar do carpo. A avaliação clínica pós-operatória consistiu na medição das amplitudes articulares do punho, escala visual analógica (EVA) e score Disabilities of the Arm, Shoulder and Hand (DASH).\n Resultados Foram incluídos quatro pacientes, dois com Madelung idiopática e dois com displasia óssea, todos do sexo feminino e com doença bilateral. Foram operados 6 punhos, a idade mediana à data de cirurgia foi 15,5 anos, e o tempo mediano de seguimento pós-operatório foi de 37,5 meses. Na análise radiográfica pós-operatória, verificou-se uma correção média de 8,8 ± 7,5° da inclinação ulnar, de 3 ± 3,9 mm do afundamento semilunar, de 8,2 ± 6,6° do ângulo da fossa semilunar e de 4,7 ± 2,6 mm do desvio palmar do carpo. Na avaliação da amplitude articular média pós-operatória, registrou-se uma flexão de 75,8 ± 3,4°; extensão de 62,5 ± 14,1°; desvio radial de 25,7 ± 2,9°; desvio cubital de 40,0 ± 2,9; pronação de 88,3 ± 2,4°; supinação de 82,5 ± 2,5°. Registou-se EVA mediana para dor residual = 1, défice funcional = 0, prejuízo estético = 0, e recomendação de procedimento cirúrgico = 10. A mediana do score DASH foi 0.\n Conclusão O tratamento da deformidade de Madelung através da osteotomia em cúpula do rádio distal e secção do ligamento de Vickers permite obter um excelente resultado estético e funcional.","mimetype":"application/xml+jats"}],"refs":[{"index":0,"extra":{"authors":["A E Flatt"],"volume-title":"The Care of Congenital Hand Anomalies"},"key":"ref1","year":1994,"container_name":"The Care of Congenital Hand Anomalies"},{"index":1,"extra":{"authors":["A Peymani"],"doi":"10.1177/1558944718793179","issue":"06","volume":"14"},"key":"ref2","year":2019,"container_name":"Hand (N Y)","title":"Surgical Management of Madelung Deformity: A Systematic Review","locator":"725"},{"index":2,"extra":{"authors":["A S Arora"],"doi":"10.1016/j.jhsa.2005.09.001","issue":"02","volume":"31"},"key":"ref3","year":2006,"container_name":"J Hand Surg Am","title":"Madelung and the recognition of Madelung's deformity","locator":"177"},{"index":3,"extra":{"authors":["D Vickers"],"doi":"10.1016/s0266-7681(05)80262-1","issue":"04","volume":"17"},"key":"ref4","year":1992,"container_name":"J Hand Surg Br","title":"Madelung deformity: surgical prophylaxis (physiolysis) during the late growth period by resection of the dyschondrosteosis lesion","locator":"401"},{"index":4,"extra":{"authors":["H K Kim"],"doi":"10.1007/s00247-009-1293-7","issue":"11","volume":"39"},"key":"ref5","year":2009,"container_name":"Pediatr Radiol","title":"Madelung deformity with Vickers ligament","locator":"1251"},{"index":5,"extra":{"authors":["E J Knutsen"],"doi":"10.1007/s11552-014-9633-y","issue":"03"},"key":"ref6","year":2014,"container_name":"Hand (N Y)","title":"Madelung's Deformity","locator":"289"},{"index":6,"extra":{"authors":["F B dos Reis"],"doi":"10.1302/0301-620x.80b5.0800817","issue":"05","volume":"80"},"key":"ref7","year":1998,"container_name":"J Bone Joint Surg Br","title":"Osteotomy of the radius and ulna for the Madelung deformity","locator":"817"},{"index":7,"extra":{"authors":["P S Fagg"],"doi":"10.1016/0266-7681(88)90042-3","issue":"01","volume":"13"},"key":"ref8","year":1988,"container_name":"J Hand Surg Br","title":"Wrist pain in the Madelung's deformity of dyschondrosteosis","locator":"11"},{"index":8,"extra":{"authors":["S Houshian"],"doi":"10.1302/0301-620x.86b4.14687","issue":"04","volume":"86"},"key":"ref9","year":2004,"container_name":"J Bone Joint Surg Br","title":"Correction of Madelung's deformity by the Ilizarov technique","locator":"536"},{"index":9,"extra":{"authors":["A Henry"],"doi":"10.1302/0301-620x.49b1.66","issue":"01","volume":"49"},"key":"ref10","year":1967,"container_name":"J Bone Joint Surg Br","title":"Madelung's deformity. A clinical and cytogenetic study","locator":"66"},{"index":10,"extra":{"authors":["V Belin"],"doi":"10.1038/ng0198-67","issue":"01","volume":"19"},"key":"ref11","year":1998,"container_name":"Nat Genet","title":"SHOX mutations in dyschondrosteosis (Leri-Weill syndrome)","locator":"67"},{"index":11,"extra":{"authors":["M Clement-Jones"],"doi":"10.1093/hmg/9.5.695","issue":"05"},"key":"ref12","year":2000,"container_name":"Hum Mol Genet","title":"The short stature homeobox gene SHOX is involved in skeletal abnormalities in Turner syndrome","locator":"695"},{"index":12,"extra":{"authors":["R P Schwartz"],"doi":"10.1016/s0022-3476(00)90028-3","issue":"04","volume":"136"},"key":"ref13","year":2000,"container_name":"J Pediatr","title":"Madelung's deformity as a presenting sign of Turner's syndrome","locator":"563"},{"index":13,"extra":{"authors":["H R McCarroll Jr"],"doi":"10.1016/j.jhsa.2010.02.003","issue":"05","volume":"35"},"key":"ref14","year":2010,"container_name":"J Hand Surg Am","title":"Madelung's deformity: diagnostic thresholds of radiographic measurements","locator":"807"},{"index":14,"extra":{"authors":["M Dannenberg"],"volume":"42"},"key":"ref15","year":1939,"container_name":"AJR Am J Roentgenol","title":"Madelung's Deformity: consideration of its roentgenological diagnostic criteria","locator":"671"},{"index":15,"extra":{"authors":["C M Steyers"],"doi":"10.1016/0363-5023(89)90175-5","issue":"04","volume":"14"},"key":"ref16","year":1989,"container_name":"J Hand Surg Am","title":"Measuring ulnar variance: a comparison of techniques","locator":"607"},{"index":16,"extra":{"authors":["P M Waters"],"volume-title":"Pediatric Hand and Upper Limb Surgery"},"key":"ref17","year":2012,"container_name":"Pediatric Hand and Upper Limb Surgery"},{"index":17,"extra":{"authors":["B Schmidt-Rohlfing"],"issue":"04","volume":"10"},"key":"ref19","year":2001,"container_name":"J Pediatr Orthop B","title":"Madelung deformity: clinical features, therapy and results","locator":"344"},{"index":18,"extra":{"authors":["L O Langer"],"doi":"10.2214/ajr.95.1.178","volume":"95"},"key":"ref20","year":1965,"container_name":"Am J Roentgen Radium Ther. Nucl Med (Stuttg)","title":"Dyschondrosteosis, a heritable bone dysplasia with characteristic roentgenographic features","locator":"178"},{"index":19,"extra":{"authors":["L P Zebala"],"doi":"10.1016/j.jhsa.2007.08.012","issue":"09","volume":"32"},"key":"ref21","year":2007,"container_name":"J Hand Surg Am","title":"Madelung's deformity: a spectrum of presentation","locator":"1393"},{"index":20,"extra":{"authors":["R Luchetti"],"doi":"10.1016/0266-7681(88)90044-7","issue":"01","volume":"13"},"key":"ref22","year":1988,"container_name":"J Hand Surg Br","title":"Carpal tunnel syndrome in Madelung's deformity","locator":"19"},{"index":21,"extra":{"authors":["I Schulstad"],"doi":"10.3109/02844317109042957","issue":"02"},"key":"ref23","year":1971,"container_name":"Scand J Plast Reconstr Surg","title":"Madelung's deformity with extensor tendon rupture. Case report","locator":"153"},{"index":22,"extra":{"authors":["B J Harley"],"doi":"10.1016/j.jhsa.2006.07.012","issue":"09","volume":"31"},"key":"ref24","year":2006,"container_name":"J Hand Surg Am","title":"Volar ligament release and distal radius dome osteotomy for correction of Madelung's deformity","locator":"1499"},{"index":23,"extra":{"authors":["P R Carter"],"issue":"04","volume":"16"},"key":"ref25","year":2000,"container_name":"Hand Clin","title":"Madelung's deformity. Surgical correction through the anterior approach","locator":"713"},{"index":24,"extra":{"authors":["S Steinman"],"doi":"10.2106/jbjs.l.00714","issue":"13","volume":"95"},"key":"ref26","year":2013,"container_name":"J Bone Joint Surg Am","title":"Volar ligament release and distal radial dome osteotomy for the correction of Madelung deformity: long-term follow-up","locator":"1198"},{"index":25,"extra":{"authors":["S Farr"],"doi":"10.1097/bpo.0000000000000434","issue":"03","volume":"36"},"key":"ref27","year":2016,"container_name":"J Pediatr Orthop","title":"Radiographic Criteria for undergoing an ulnar shortening osteotomy in Madelung deformity: A long-term experience from a single institution","locator":"310"},{"index":26,"extra":{"authors":["J E Otte"],"doi":"10.1016/j.jhsa.2018.04.033","issue":"02","volume":"44"},"key":"ref28","year":2019,"container_name":"J Hand Surg Am","title":"Treatment of Madelung deformity with Vicker ligament release and radial physiolyses: a case series","locator":"158.e1"}],"contribs":[{"index":0,"creator_id":"id5alwh4vjetjkupm55rhcnijq","creator":{"orcid":"0000-0002-9349-2483","surname":"Carvalho","given_name":"Marcos","display_name":"Marcos Carvalho","state":"active","ident":"id5alwh4vjetjkupm55rhcnijq","revision":"2eaa4291-1a97-43ad-819e-6712bab305a0"},"raw_name":"Marcos Carvalho","given_name":"Marcos","surname":"Carvalho","role":"author","raw_affiliation":"Serviço de Ortopedia Pediátrica, Hospital Pediátrico, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal"},{"index":1,"raw_name":"Pedro Sá Cardoso","given_name":"Pedro Sá","surname":"Cardoso","role":"author","raw_affiliation":"Serviço de Ortopedia Pediátrica, Hospital Pediátrico, Centro Hospitalar e Universitário de Coimbra, Coimbra, Portugal"},{"index":2,"raw_name":"Cristina Alves","given_name":"Cristina","surname":"Alves","role":"author","raw_affiliation":"Serviço de Ortopedia Pediátrica, Hospital Pediátrico, Centro Hospitalar e Universitário de Coimbra, 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